RT Book, Section
A1 Lichtman, Marshall A.
A1 Kaushansky, Kenneth
A1 Kipps, Thomas J.
A1 Prchal, Josef T.
A1 Levi, Marcel M.
SR Print(0)
ID 1126651065
T1 Congenital Dyserythropoietic Anemias
T2 Williams Manual of Hematology, 8e
YR 2011
FD 2011
PB McGraw-Hill Education
PP New York, NY
SN 9780071622424
LK hemonc.mhmedical.com/content.aspx?aid=1126651065
RD 2024/04/19
AB Congenital  dyserythropoietic  anemias  (CDA)  are  a  heterogeneous  group  of  disorders  characterized  by  anemia,  the  presence  of  multinuclear  erythroid  precursors  in  the  marrow,  ineffective  erythropoiesis,  and  iron  overload.Although  rare,  uncovering  the  molecular  basis  of  CDA  has  helped  unravel  novel  aspects  of  the  cell  biology  of  erythropoiesis.Three  types  of  CDA  have  been  distinguished.  In  addition,  a  number  of  patients  with  forms  of  congenital  dyserythropoietic  anemia  that  do  not  fit  these  categories  have  been  described.